Atormac
Home  -  About us  -  Editorial board  -  Search  -  Ahead of print  -  Current issue  -  Archives  -  Instructions  -  Subscribe  -  Contacts  -  Advertise - Login 
 
 
     
CASE REPORT - SURGICAL PATHOLOGY
Year : 2013  |  Volume : 3  |  Issue : 2  |  Page : 192-194

Primary peripheral primitive neuroectodermal tumor of the mandible


1 Department of Surgical Oncology, Cancer Institute (Women's India Association), Adyar, Chennai, Tamil Nadu, India
2 Department of Preventive Oncology, Cancer Institute (Women's India Association), Adyar, Chennai, Tamil Nadu, India
3 Department of Pathology, Cancer Institute (Women's India Association), Adyar, Chennai, Tamil Nadu, India

Correspondence Address:
Arvind Krishnamurthy
Department of Surgical Oncology, Cancer Institute (Women's India Association), 36, Sardar Patel Rd, Adyar, Chennai - 600 020, Tamil Nadu
India
Login to access the Email id


DOI: 10.4103/2231-0746.119219

PMID: 24205482

Rights and Permissions

Primitive neuroectodermal tumor (PNET) is a broad term that includes a wide array of lesions with varying differentiating potential affecting both the central and peripheral nervous system. Peripheral PNET (pPNET), a variant of PNET, is known to arise in many places throughout the body; involvement of the mandible is however rare. A review of the scientific literature describes only seven reports of pPNET to be arising from the mandible. Given their insidious clinical symptoms, variable locations and rarity, the accurate diagnosis of peripheral PNETs poses a challenge for clinicians. PNETs exhibits characteristic immunophenotypical and genetic features that distinguish them from other small round cell tumors. A multidisciplinary approach is necessary to manage patients affected by PNET. There is however no consensus about the best therapeutic strategy. We recently got to treat a young patient with mandibular PNET; the clinical course as well as the histopathology with immunohistochemistry correlation of this rare entity is discussed.


[FULL TEXT] [PDF]*
Print this article     Email this article
 Next article
 Previous article
 Table of Contents

 Similar in PUBMED
   Search Pubmed for
   Search in Google Scholar for
 Related articles
 Citation Manager
 Access Statistics
 Reader Comments
 Email Alert *
 Add to My List *
 * Requires registration (Free)
 

 Article Access Statistics
    Viewed2032    
    Printed75    
    Emailed0    
    PDF Downloaded291    
    Comments [Add]    

Recommend this journal